CT-histologic correlation of the ATS/ERS 2002 classification of idiopathic interstitial pneumonias. ADVERTISEMENT: Radiopaedia is free thanks to our supporters and advertisers. Lynch DA, Sverzellati N, Travis WD, Brown KK, Colby TV, Galvin JR, Goldin JG, Hansell DM, Inoue Y, Johkoh T, Nicholson AG, Knight SL, Raoof S, Richeldi L, Ryerson CJ, Ryu JH, Wells AU. 4. 2002;22 Spec No : S151-65. The spectrum of conditions included is broad, ranging from occasional self-limited inflammatory processes to severe debilitating fibrosis of the lungs. d Interstitial lung disease in association with connective tissue disorder has a better prognosis than idiopathic counterparts. Interstitial lung disease (ILD), or diffuse parenchymal lung disease (DPLD), is a group of lung diseases affecting the interstitium (the tissue and space around the alveoli (air sacs of the lungs). Chest radiography is frequently the initial indicator of an ILD, and comparison of radiographs taken at different time points can show the rate of disease progression. Interstitial (in-tur-STISH-ul) lung disease describes a large group of disorders, most of which cause progressive scarring of lung tissue. {"url":"/signup-modal-props.json?lang=us\u0026email="}, {"containerId":"expandableQuestionsContainer","displayRelatedArticles":true,"displayNextQuestion":true,"displaySkipQuestion":true,"articleId":60014,"mcqUrl":"https://radiopaedia.org/articles/diagnostic-hrct-criteria-for-usual-interstitial-pneumonia-uip-pattern-fleischner-society-guideline-2018/questions/1579?lang=us"}. Smoking-related interstitial lung disease: radiologic-clinical-pathologic correlation. Interstitial lung disease is considered a misnomer by some, as many of the diseases also involve the alveolar spaces. These disorders are classified together because of overlapping clinical, radiographic, physiologic, or pathologic manifestations. It concerns alveolar epithelium, pulmonary capillary endothelium, basement membrane, and perivascular and perilymphatic tissues. Radiographics. eCollection 2018. Interpret the significance of 'early interstitial abnormality' on CT. Some types of autoimmune diseases, such as rheumatoid … J Cancer. However, this approach has yet to be implemented in ILD. A number of precipitants can cause diffuse interstitial disease such as: Eliciting a history of underlying systemic disease is also helpful since they may involve the lungs in a diffuse and infiltrative manner. 2012;199 (4): W464-76. Interstitial lung disease (ILD) refers to a broad category of diffuse parenchymal lung diseases characterized by inflammation and/or fibrosis of the lungs. What every radiologist should know about idiopathic interstitial pneumonias. Hypersensitivity pneumonitis (HP) is a complex fibroinflammatory lung condition that arises from repeated exposure, usually to aerosolised organic antigens, in sensitised individuals. {"url":"/signup-modal-props.json?lang=us\u0026email="}, anti-Jo-1 antibody positive interstitial lung disease, interstitial pneumonia with autoimmune features, non-specific interstitial pneumonia (NSIP), respiratory bronchiolitis-interstitial lung disease (RB-ILD), desquamative interstitial pneumonia (DIP), combined pulmonary fibrosis and emphysema (CPFE), All Idiopathic Chronic Lung Diseases aRe Nonspecific, acute unilateral airspace opacification (differential), acute bilateral airspace opacification (differential), acute airspace opacification with lymphadenopathy (differential), chronic unilateral airspace opacification (differential), chronic bilateral airspace opacification (differential), osteophyte induced adjacent pulmonary atelectasis and fibrosis, pediatric chest x-ray in the exam setting, normal chest x-ray appearance of the diaphragm, posterior tracheal stripe/tracheo-esophageal stripe, obliteration of the retrosternal airspace, leflunomide-induced acute interstitial pneumonia, fibrotic non-specific interstitial pneumonia, cellular non-specific interstitial pneumonia, respiratory bronchiolitis–associated interstitial lung disease, diagnostic HRCT criteria for UIP pattern - ATS/ERS/JRS/ALAT (2011), diagnostic HRCT criteria for UIP pattern - Fleischner society guideline (2018)​, domestically acquired particulate lung disease, lepidic predominant adenocarcinoma (formerly non-mucinous BAC), micropapillary predominant adenocarcinoma, invasive mucinous adenocarcinoma (formerly mucinous BAC), lung cancer associated with cystic airspaces, primary sarcomatoid carcinoma of the lung, large cell neuroendocrine cell carcinoma of the lung, squamous cell carcinoma in situ (CIS) of lung, minimally invasive adenocarcinoma of the lung, diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH), calcifying fibrous pseudotumor of the lung, IASLC (International Association for the Study of Lung Cancer) 8th edition (current), IASLC (International Association for the Study of Lung Cancer) 7th edition (superseeded), 1996 AJCC-UICC Regional Lymph Node Classification for Lung Cancer Staging, autoimmune and collagen vascular diseases. 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